Creutzfeldt-Jakob disease surveillance system (CJDSS) report
Statistics
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Statistics August 31, 2023 PDF Version (207 Kb - 4 pages)
Year of reporting | Number of referrals |
---|---|
1998 | 43 |
1999 | 63 |
2000 | 82 |
2001 | 101 |
2002 | 103 |
2003 | 75 |
2004 | 90 |
2005 | 97 |
2006 | 80 |
2007 | 101 |
2008 | 100 |
2009 | 104 |
2010 | 76 |
2011 | 102 |
2012 | 103 |
2013 | 99 |
2014 | 99 |
2015 | 98 |
2016 | 117 |
2017 | 116 |
2018 | 125 |
2019 | 142 |
2020 | 123 |
2021 | 140 |
2022 | 162 |
2023 | 101 |
Total | 2640 |
Year | Sporadic | Iatrogenic | Genetic | vCJD | Total |
---|---|---|---|---|---|
1998 | 22 | 1 | 1 | 0 | 24 |
1999 | 27 | 2 | 3 | 0 | 32 |
2000 | 32 | 0 | 3 | 0 | 35 |
2001 | 27 | 0 | 3 | 0 | 30 |
2002 | 30 | 0 | 5 | 1 | 36 |
2003 | 27 | 1 | 1 | 0 | 29 |
2004 | 42 | 0 | 4 | 0 | 44 |
2005 | 42 | 0 | 2 | 0 | 44 |
2006 | 39 | 0 | 5 | 0 | 44 |
2007 | 35 | 0 | 4 | 0 | 39 |
2008 | 48 | 0 | 1 | 0 | 49 |
2009 | 48 | 0 | 5 | 0 | 53 |
2010 | 35 | 0 | 3 | 0 | 38 |
2011 | 46 | 0 | 4 | 1 | 51 |
2012 | 62 | 0 | 1 | 0 | 63 |
2013 | 50 | 0 | 1 | 0 | 51 |
2014 | 51 | 0 | 5 | 0 | 56 |
2015 | 44 | 0 | 8 | 0 | 52 |
2016 | 57 | 1 | 6 | 0 | 64 |
2017 | 82 | 0 | 5 | 0 | 87 |
2018 | 75 | 1 | 5 | 0 | 81 |
2019 | 76 | 0 | 3 | 0 | 79 |
2020 | 65 | 0 | 4 | 0 | 69 |
2021 | 60 | 0 | 3 | 0 | 63 |
2022 | 88 | 0 | 2 | 0 | 90 |
2023 | 40 | 0 | 0 | 0 | 40 |
Total | 1250 | 6 | 85 | 2 | 1343 |
Cases with definite and probable diagnosis to date |

Text Description
CJD Cases by Province/Territory August 31, 2023 | |
---|---|
Provinces | Total CJD Cases |
Newfoundland & Labrador | 18 |
Prince Edward Island | 4 |
Nova Scotia | 45 |
New Brunswick | 43 |
Quebec | 348 |
Ontario | 468 |
Manitoba | 50 |
Saskatchewan | 46 |
Alberta | 136 |
British Columbia | 183 |
Yukon | 2 |
Northwest Territories | 0.0 |
Nunavut | 0.0 |
National total: 1343
Provincial totals of definite & probable CJD
*Canadian CJD surveillance began in 1998
Return to CJD Cases by Province/Territory 31 July, 2023
Year of death | Total CJD cases | Population of Canada | Crude mortality rate |
---|---|---|---|
1998 | 24 | 30,244,982 | 0.79 |
1999 | 32 | 30,492,106 | 1.05 |
2000 | 35 | 30,783,969 | 1.14 |
2001 | 30 | 31,130,030 | 0.96 |
2002 | 36 | 31,450,443 | 1.14 |
2003 | 29 | 31,734,851 | 0.91 |
2004 | 44 | 32,037,434 | 1.37 |
2005 | 44 | 32,352,233 | 1.36 |
2006 | 44 | 32,678,986 | 1.35 |
2007 | 39 | 33,001,076 | 1.18 |
2008 | 49 | 33,371,810 | 1.47 |
2009 | 53 | 33,756,714 | 1.57 |
2010 | 38 | 34,131,451 | 1.11 |
2011 | 51 | 34,472,304 | 1.48 |
2012 | 63 | 34,880,248 | 1.81 |
2013 | 51 | 35,289,003 | 1.45 |
2014 | 56 | 35,675,834 | 1.57 |
2015 | 52 | 35,702,707 | 1.46 |
2016 | 64 | 36,286,400 | 1.76 |
2017 | 86 | 36,712,658 | 2.37 |
2018 | 80 | 37,589,262 | 2.15 |
2019 | 79 | 37,811,399 | 2.09 |
2020 | 69 | 38,033,014 | 1.81 |
2021 | 63 | 38,929,902 | 1.62 |
2022 | 90 | 39,292,355 | 2.31 |
Cases with definite and probable diagnosis to date Population estimates as of Q3 2022 (Statistics Canada population estimates, quarterly) |
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