Creutzfeldt-Jakob disease surveillance system (CJDSS) report

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Statistics August 31, 2025 PDF Version (502 KB - 4 pages)

Definite and probable CJD, 1998-2025
As of August 31, 2025
Year	Sporadic	Iatrogenic	Genetic	vCJD	Total
1998	22	1	1	0	24
1999	27	2	3	0	32
2000	32	0	3	0	35
2001	27	0	3	0	30
2002	31	0	4	1	36
2003	27	1	1	0	29
2004	42	0	2	0	44
2005	42	0	2	0	44
2006	39	0	5	0	44
2007	35	0	4	0	39
2008	48	0	1	0	49
2009	48	0	5	0	53
2010	35	0	3	0	38
2011	46	0	4	1	51
2012	63	0	1	0	64
2013	50	0	1	0	51
2014	52	0	4	0	56
2015	43	0	9	0	52
2016	61	1	6	0	68
2017	83	0	8	0	91
2018	76	1	6	0	83
2019	76	0	6	0	82
2020	68	0	4	0	72
2021	61	0	5	0	66
2022	93	0	3	0	96
2023	74	0	2	0	76
2024	70	0	3	0	73
2025	28	0	1	0	29
Total	1,399	6	100	2	1,507
Cases with definite and probable diagnosis to date Variant CJD (vCJD) The CJDSS uses current, internationally accepted diagnostic criteria (PDF, 252 KB) to classify definite and probable cases of CJD in Canada.

CJD deaths in Canada
Year of death	Total CJD cases	Population of Canada	Crude mortality rate
1998	24	30,244,982	0.79
1999	32	30,492,106	1.05
2000	35	30,783,969	1.14
2001	30	31,130,030	0.96
2002	36	31,450,443	1.14
2003	29	31,734,851	0.91
2004	44	32,037,434	1.37
2005	44	32,352,233	1.36
2006	44	32,678,986	1.35
2007	39	33,001,076	1.18
2008	49	33,371,810	1.47
2009	53	33,756,714	1.57
2010	38	34,131,451	1.11
2011	51	34,472,304	1.48
2012	64	34,880,248	1.83
2013	51	35,289,003	1.45
2014	56	35,675,834	1.57
2015	52	35,702,707	1.46
2016	66	36,286,400	1.82
2017	88	36,712,658	2.40
2018	83	37,589,262	2.21
2019	82	37,811,399	2.17
2020	72	38,033,014	1.89
2021	66	38,929,902	1.70
2022	96	39,292,355	2.44
2023	76	40,083,484	1.90
Cases with definite and probable diagnosis to date Population estimates as of Q3 (Statistics Canada population estimates, quarterly)