Creutzfeldt-Jakob Disease
CJD-Surveillance System
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Statistics
- Referrals of Suspected CJD Reported by CJDSS
- CJD Cases Reported by CJDSS
- CJD Cases Reported by Province
- Incidence of CJD Cases Reported by CJDSS in Canada
Data tables are also available in an alternate format for downloading or viewing:
Statistics: August 2017 PDF Version (963 KB - 4 pages)
| Year of Reporting | Number of Referrals |
|---|---|
| 1997 | 4 |
| 1998 | 43 |
| 1999 | 63 |
| 2000 | 82 |
| 2001 | 101 |
| 2002 | 103 |
| 2003 | 75 |
| 2004 | 90 |
| 2005 | 97 |
| 2006 | 80 |
| 2007 | 101 |
| 2008 | 100 |
| 2009 | 104 |
| 2010 | 76 |
| 2011 | 102 |
| 2012 | 103 |
| 2013 | 99 |
| 2014 | 99 |
| 2015 | 98 |
| 2016 | 116 |
| 2017 | 81 |
| Total | 1817 |
| Deaths of Definite and Probable CJD | |||||||
| Year | Sporadic | Iatrogenic | Familial | GSS | FFI | vCJD | Total |
|---|---|---|---|---|---|---|---|
| Cases with definite & probable diagnosis to date. | |||||||
| 1994 | 2 | 0 | 0 | 1 | 0 | 0 | 3 |
| 1995 | 3 | 0 | 0 | 0 | 0 | 0 | 3 |
| 1996 | 13 | 0 | 0 | 0 | 0 | 0 | 13 |
| 1997 | 16 | 0 | 1 | 1 | 0 | 0 | 18 |
| 1998 | 22 | 1 | 0 | 1 | 0 | 0 | 24 |
| 1999 | 27 | 2 | 2 | 1 | 0 | 0 | 32 |
| 2000 | 32 | 0 | 0 | 3 | 0 | 0 | 35 |
| 2001 | 27 | 0 | 2 | 1 | 0 | 0 | 30 |
| 2002 | 31 | 0 | 2 | 2 | 0 | 1 | 36 |
| 2003 | 27 | 1 | 1 | 0 | 0 | 0 | 29 |
| 2004 | 42 | 0 | 1 | 1 | 0 | 0 | 44 |
| 2005 | 42 | 0 | 1 | 1 | 0 | 0 | 44 |
| 2006 | 39 | 0 | 1 | 3 | 1 | 0 | 44 |
| 2007 | 35 | 0 | 0 | 4 | 0 | 0 | 39 |
| 2008 | 48 | 0 | 1 | 0 | 0 | 0 | 49 |
| 2009 | 48 | 0 | 3 | 2 | 0 | 0 | 53 |
| 2010 | 35 | 0 | 3 | 0 | 0 | 0 | 38 |
| 2011 | 46 | 0 | 3 | 1 | 0 | 1 | 51 |
| 2012 | 62 | 0 | 1 | 0 | 0 | 0 | 63 |
| 2013 | 50 | 0 | 0 | 0 | 1 | 0 | 51 |
| 2014 | 51 | 0 | 4 | 0 | 1 | 0 | 56 |
| 2015 | 44 | 0 | 5 | 1 | 2 | 0 | 52 |
| 2016 | 49 | 1 | 3 | 1 | 0 | 0 | 54 |
| 2017 | 27 | 0 | 0 | 1 | 0 | 0 | 28 |
| Total | 818 | 5 | 34 | 25 | 5 | 2 | 889 |
CJD Cases by Province/Territory August 31, 2017
Text Equivalent - CJD Cases by Province/Territory August 31, 2017
| Provinces | Total CJD Cases | CJD Cases % | % Expected (Difference) |
|---|---|---|---|
Actual CJD n=889 |
|||
Newfoundland & Labrador |
17 |
1.9 |
130.9% |
Prince Edward Island |
2 |
0.2 |
54.9% |
Nova Scotia |
34 |
3.8 |
146.2% |
New Brunswick |
24 |
2.7 |
129.4% |
Quebec |
213 |
24.0 |
104.4% |
Ontario |
320 |
36.0 |
93.4% |
Manitoba |
38 |
4.3 |
117.7% |
Saskatchewan |
36 |
4.0 |
127.7% |
Alberta |
89 |
10.0 |
85.4% |
British Columbia |
116 |
13.0 |
99.6% |
Yukon |
0.0 |
0.0 |
0.0% |
Northwest Territories |
0.0 |
0.0 |
0.0% |
Nunavut |
0.0 |
0.0 |
0.0% |
| Year of Death | Total CJD Cases | Population of Canada | Incidence Rate |
|---|---|---|---|
| Cases with definite & probable diagnosis to date. 2016 Population, Source: Demography Division, Statistics Canada |
|||
| 1999 | 32 | 30,492,106 | 1.05 |
| 2000 | 35 | 30,783,969 | 1.14 |
| 2001 | 30 | 31,130,030 | 0.96 |
| 2002 | 36 | 31,450,443 | 1.14 |
| 2003 | 29 | 31,734,851 | 0.91 |
| 2004 | 44 | 32,037,434 | 1.37 |
| 2005 | 44 | 32,352,233 | 1.36 |
| 2006 | 44 | 32,678,986 | 1.35 |
| 2007 | 39 | 33,001,076 | 1.18 |
| 2008 | 49 | 33,371,810 | 1.47 |
| 2009 | 53 | 33,756,714 | 1.57 |
| 2010 | 38 | 34,131,451 | 1.11 |
| 2011 | 51 | 34,472,304 | 1.48 |
| 2012 | 63 | 34,880,248 | 1.81 |
| 2013 | 51 | 35,289,003 | 1.45 |
| 2014 | 56 | 35,675,834 | 1.57 |
| 2015 | 52 | 35,702,707 | 1.46 |
| 2016 | 54 | 36,286,400 | 1.49 |
| 2017 | 28 | 36,546,956 | 1.15 |
World Wide average occurrence of CJD is approximately 1-2 per million population
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