Creutzfeldt-Jakob Disease Surveillance System Report

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Referrals of Suspected CJD Reported by CJDSS, 1997-2017
As of November 30, 2017
Year of Reporting Number of Referrals
1997 4
1998 43
1999 63
2000 82
2001 101
2002 103
2003 75
2004 90
2005 97
2006 80
2007 101
2008 100
2009 104
2010 76
2011 102
2012 103
2013 99
2014 99
2015 98
2016 117
2017 105
Total 1842
CJD Deaths Reported by CJDSS, 1994-2017
As of November 30, 2017

Deaths of Definite and Probable CJD

Year Sporadic Iatrogenic Familial GSS FFI vCJD Total
1994 2 0 0 1 0 0 3
1995 3 0 0 0 0 0 3
1996 13 0 0 0 0 0 13
1997 16 0 1 1 0 0 18
1998 22 1 0 1 0 0 24
1999 27 2 2 1 0 0 32
2000 32 0 0 3 0 0 35
2001 27 0 2 1 0 0 30
2002 31 0 2 2 0 1 36
2003 27 1 1 0 0 0 29
2004 42 0 1 1 0 0 44
2005 42 0 1 1 0 0 44
2006 39 0 1 3 1 0 44
2007 35 0 0 4 0 0 39
2008 48 0 1 0 0 0 49
2009 48 0 3 2 0 0 53
2010 35 0 3 0 0 0 38
2011 46 0 3 1 0 1 51
2012 62 0 1 0 0 0 63
2013 50 0 0 0 1 0 51
2014 51 0 4 0 1 0 56
2015 44 0 5 1 2 0 52
2016 51 1 3 1 0 0 58
2017 41 0 0 1 0 0 43
Total 834 5 36 25 6 2 908

Cases with definite & probable diagnosis to date.

CJD Cases by Province/Territory November 30, 2017
Map of CJD Cases by Province/Territory November 30, 2017
CJD Cases by Province/Territory November 30, 2017 - Text version
CJD Cases by Province/Territory November 30, 2017
Provinces Total CJD Casesfigure table note 1 CJD Cases %figure table note 2 % Expected (Difference)figure table note 3
Newfoundland & Labrador 17 1.9 128.2%
Prince Edward Island 2 0.2 53.8%
Nova Scotia 35 3.9 147.3%
New Brunswick 25 2.8 132.0%
Quebec 219 24.1 105.1%
Ontario 325 35.8 92.9%
Manitoba 38 4.2 115.2%
Saskatchewan 36 4.0 125.0%
Alberta 91 10.0 85.5%
British Columbia 120 13.2 100.9%
Yukon 0.0 0.0 0.0%
Northwest Territories 0.0 0.0 0.0%
Nunavut 0.0 0.0 0.0%
Figure table notes
Figure table note 1

Actual CJD n=908

Return to figure table note 1 referrer

Figure table note 2

Actual % CJD

Return to figure table note 2 referrer

Figure table note 3

% of Predicted CJD (based on 2016 population)

Return to figure table note 3 referrer

Data includes both deceased and alive cases

Incidence of CJD Deaths Reported by CJDSS in Canada
As of November 30, 2017
Year of Death Total CJD Cases Population of Canada Incidence Rate
1999 32 30,492,106 1.05
2000 35 30,783,969 1.14
2001 30 31,130,030 0.96
2002 36 31,450,443 1.14
2003 29 31,734,851 0.91
2004 44 32,037,434 1.37
2005 44 32,352,233 1.36
2006 44 32,678,986 1.35
2007 39 33,001,076 1.18
2008 49 33,371,810 1.47
2009 53 33,756,714 1.57
2010 38 34,131,451 1.11
2011 51 34,472,304 1.48
2012 63 34,880,248 1.81
2013 51 35,289,003 1.45
2014 56 35,675,834 1.57
2015 52 35,702,707 1.46
2016 58 36,286,400 1.60
2017 43 36,546,956 1.28

Cases with definite & probable diagnosis to date.

2016 Population, Source: Demography Division, Statistics Canada

World Wide average occurrence of CJD is approximately 1-2 per million population

European Creutzfeldt Jakob Disease Surveillance Network

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