Creutzfeldt-Jakob disease surveillance system (CJDSS) report

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Statistics October 31, 2025 PDF Version (207 KB - 4 pages)

Referrals of suspected CJD reported by CJDSS, 1998-2025
As of October 31, 2025
Year of reporting	Number of referrals
1998	43
1999	63
2000	82
2001	101
2002	103
2003	75
2004	90
2005	97
2006	80
2007	101
2008	100
2009	104
2010	76
2011	102
2012	103
2013	99
2014	99
2015	98
2016	117
2017	116
2018	125
2019	142
2020	123
2021	140
2022	162
2023	146
2024	155
2025	115
Total	2,957
Note: The data presented in this table are subject to ongoing revision. Cases may be added, updated, or removed due to case re-classification or historical data cleaning

Definite and probable CJD, 1998-2025
As of October 31, 2025
Year	Sporadic	Iatrogenic	Genetic	vCJD	Total
1998	22	1	1	0	24
1999	27	2	3	0	32
2000	32	0	3	0	35
2001	27	0	3	0	30
2002	31	0	4	1	36
2003	27	1	1	0	29
2004	42	0	2	0	44
2005	42	0	2	0	44
2006	39	0	5	0	44
2007	35	0	4	0	39
2008	48	0	1	0	49
2009	48	0	5	0	53
2010	35	0	3	0	38
2011	46	0	4	1	51
2012	64	0	1	0	65
2013	50	0	1	0	51
2014	52	0	4	0	56
2015	43	0	9	0	52
2016	62	1	7	0	70
2017	83	0	7	0	90
2018	76	1	5	0	81
2019	76	0	6	0	82
2020	70	0	4	0	74
2021	61	0	5	0	66
2022	95	0	3	0	96
2023	75	0	3	0	78
2024	68	0	3	0	71
2025	44	0	4	0	49
Total	1,419	6	104	2	1,531
Cases with definite and probable diagnosis to date. Variant CJD (vCJD) The CJDSS uses current, internationally accepted diagnostic criteria (PDF, 252 KB) to classify definite and probable cases of CJD in Canada. Note: The data presented in this table are subject to ongoing revision. Cases may be added, updated or removed due to case re-classification or historical data cleaning.

CJD deaths in Canada
Year of death	Total CJD cases	Population of Canada	Crude mortality rate
1998	24	30,244,982	0.79
1999	32	30,492,106	1.05
2000	35	30,783,969	1.14
2001	30	31,130,030	0.96
2002	36	31,450,443	1.14
2003	29	31,734,851	0.91
2004	44	32,037,434	1.37
2005	44	32,352,233	1.36
2006	44	32,678,986	1.35
2007	39	33,001,076	1.18
2008	49	33,371,810	1.47
2009	53	33,756,714	1.57
2010	38	34,131,451	1.11
2011	51	34,472,304	1.48
2012	65	34,880,248	1.86
2013	51	35,289,003	1.45
2014	56	35,675,834	1.57
2015	52	35,702,707	1.46
2016	70	36,286,400	1.93
2017	90	36,712,658	2.45
2018	81	37,589,262	2.15
2019	82	37,811,399	2.17
2020	74	38,033,014	1.95
2021	66	38,929,902	1.70
2022	98	39,292,355	2.49
2023	78	40,083,484	1.95
2024	71	41,465,298	1.71
Cases with definite and probable diagnosis to date. Population estimates as of Q3 (Statistics Canada population estimates, quarterly). Note: The data presented in this table are subject to ongoing revision. Cases may be added, updated, or removed due to case re-classification or historical data cleaning.

2025-11-17