Creutzfeldt-Jakob disease surveillance system report

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Definite and probable CJD, 1998-2021
As of October 31, 2021
Year	Sporadic	Iatrogenic	Familial	GSS	FFI	vCJD	Total
1998	22	1	0	1	0	0	24
1999	27	2	2	1	0	0	32
2000	32	0	0	3	0	0	35
2001	27	0	2	1	0	0	30
2002	31	0	2	2	0	1	36
2003	27	1	1	0	0	0	29
2004	42	0	1	1	0	0	44
2005	42	0	1	1	0	0	44
2006	39	0	1	3	1	0	44
2007	35	0	0	4	0	0	39
2008	48	0	1	0	0	0	49
2009	48	0	3	2	0	0	53
2010	35	0	3	0	0	0	38
2011	46	0	3	1	0	1	51
2012	62	0	1	0	0	0	63
2013	50	0	0	0	1	0	51
2014	51	0	4	0	1	0	56
2015	44	0	5	1	2	0	52
2016	57	1	5	1	0	0	64
2017	82	0	2	1	1	0	87
2018	75	1	4	0	1	0	81
2019	76	0	2	0	0	0	78
2020	61	0	4	0	0	0	65
2021	16	0	0	1	0	0	17
Total	1075	6	47	23	7	2	1162
Cases with definite and probable diagnosis to date. Gerstmann-Sträussler-Scheinker disease (GSS) Fatal familial insomnia (FFI) Variant CJD (vCJD)

Provinces	Total CJD cases^{figure table note 1}
Newfoundland & Labrador	18
Prince Edward Island	2
Nova Scotia	38
New Brunswick	37
Quebec	286
Ontario	407
Manitoba	47
Saskatchewan	40
Alberta	119
British Columbia	167
Yukon	1.0
Northwest Territories	0.0
Nunavut	0.0
National total: 1162 Canadian CJD surveillance began in 1998 Figure table note 1 Provincial totals of definite and probable CJD Return to figure table note 1 referrer

CJD deaths in Canada
Year of death	Total CJD cases	Population of Canada	Crude mortality rate
1998	24	30,244,982	0.79
1999	32	30,492,106	1.05
2000	35	30,783,969	1.14
2001	30	31,130,030	0.96
2002	36	31,450,443	1.14
2003	29	31,734,851	0.91
2004	44	32,037,434	1.37
2005	44	32,352,233	1.36
2006	44	32,678,986	1.35
2007	39	33,001,076	1.18
2008	49	33,371,810	1.47
2009	53	33,756,714	1.57
2010	38	34,131,451	1.11
2011	51	34,472,304	1.48
2012	63	34,880,248	1.81
2013	51	35,289,003	1.45
2014	56	35,675,834	1.57
2015	52	35,702,707	1.46
2016	64	36,286,400	1.76
2017	86	36,712,658	2.34
2018	80	37,589,262	2.13
2019	78	37,802,043	2.06
Cases with definite and probable diagnosis to date Population estimates as of July each year (Statistics Canada population estimates, quarterly)