Creutzfeldt-Jakob Disease

Data tables are also available in an alternate format for downloading or viewing:
Statistics: August 2017 PDF Version (963 KB - 4 pages)

Referrals of Suspected CJD Reported by CJDSS, 1997-2017
As of August 31, 2017
Year of Reporting Number of Referrals
1997 4
1998 43
1999 63
2000 82
2001 101
2002 103
2003 75
2004 90
2005 97
2006 80
2007 101
2008 100
2009 104
2010 76
2011 102
2012 103
2013 99
2014 99
2015 98
2016 116
2017 81
Total 1817
CJD Deaths Reported by CJDSS, 1994-2017
As of August 31, 2017
Deaths of Definite and Probable CJD
Year Sporadic Iatrogenic Familial GSS FFI vCJD Total
Cases with definite & probable diagnosis to date.
1994 2 0 0 1 0 0 3
1995 3 0 0 0 0 0 3
1996 13 0 0 0 0 0 13
1997 16 0 1 1 0 0 18
1998 22 1 0 1 0 0 24
1999 27 2 2 1 0 0 32
2000 32 0 0 3 0 0 35
2001 27 0 2 1 0 0 30
2002 31 0 2 2 0 1 36
2003 27 1 1 0 0 0 29
2004 42 0 1 1 0 0 44
2005 42 0 1 1 0 0 44
2006 39 0 1 3 1 0 44
2007 35 0 0 4 0 0 39
2008 48 0 1 0 0 0 49
2009 48 0 3 2 0 0 53
2010 35 0 3 0 0 0 38
2011 46 0 3 1 0 1 51
2012 62 0 1 0 0 0 63
2013 50 0 0 0 1 0 51
2014 51 0 4 0 1 0 56
2015 44 0 5 1 2 0 52
2016 49 1 3 1 0 0 54
2017 27 0 0 1 0 0 28
Total 818 5 34 25 5 2 889

CJD Cases by Province/Territory August 31, 2017

CJD Cases by Province/Territory August 31, 2017
Text Equivalent - CJD Cases by Province/Territory August 31, 2017
CJD Cases by Province/Territory 31 August, 2017
Provinces Total CJD Cases CJD Cases % % Expected (Difference)

Actual CJD n=889
Actual % CJD
% of Predicted CJD (based on 2016 population)
Data includes both deceased and alive cases

Newfoundland & Labrador

17

1.9

130.9%

Prince Edward Island

2

0.2

54.9%

Nova Scotia

34

3.8

146.2%

New Brunswick

24

2.7

129.4%

Quebec

213

24.0

104.4%

Ontario

320

36.0

93.4%

Manitoba

38

4.3

117.7%

Saskatchewan

36

4.0

127.7%

Alberta

89

10.0

85.4%

British Columbia

116

13.0

99.6%

Yukon

0.0

0.0

0.0%

Northwest Territories

0.0

0.0

0.0%

Nunavut

0.0

0.0

0.0%

Incidence of CJD Deaths Reported by CJDSS in Canada
As of August 31, 2017
Year of Death Total CJD Cases Population of Canada Incidence Rate
Cases with definite & probable diagnosis to date.
2016 Population, Source: Demography Division, Statistics Canada
1999 32 30,492,106 1.05
2000 35 30,783,969 1.14
2001 30 31,130,030 0.96
2002 36 31,450,443 1.14
2003 29 31,734,851 0.91
2004 44 32,037,434 1.37
2005 44 32,352,233 1.36
2006 44 32,678,986 1.35
2007 39 33,001,076 1.18
2008 49 33,371,810 1.47
2009 53 33,756,714 1.57
2010 38 34,131,451 1.11
2011 51 34,472,304 1.48
2012 63 34,880,248 1.81
2013 51 35,289,003 1.45
2014 56 35,675,834 1.57
2015 52 35,702,707 1.46
2016 54 36,286,400 1.49
2017 28 36,546,956 1.15

World Wide average occurrence of CJD is approximately 1-2 per million population

European Creutzfeldt Jakob Disease Surveillance Network

Report a problem or mistake on this page
Please select all that apply:

Privacy statement

Thank you for your help!

You will not receive a reply. For enquiries, contact us.

Date modified: