Creutzfeldt-Jakob Disease Surveillance System Report

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CJD Deaths Reported by CJDSS, 1994-2018
As of May 31 2018
Deaths of Definite and Probable CJD
Year	Sporadic	Iatrogenic	Familial	GSS	FFI	vCJD	Total
1994	2	0	0	1	0	0	3
1995	3	0	0	0	0	0	3
1996	13	0	0	0	0	0	13
1997	16	0	1	1	0	0	18
1998	22	1	0	1	0	0	24
1999	27	2	2	1	0	0	32
2000	32	0	0	3	0	0	35
2001	27	0	2	1	0	0	30
2002	31	0	2	2	0	1	36
2003	27	1	1	0	0	0	29
2004	42	0	1	1	0	0	44
2005	42	0	1	1	0	0	44
2006	39	0	1	3	1	0	44
2007	35	0	0	4	0	0	39
2008	48	0	1	0	0	0	49
2009	48	0	3	2	0	0	53
2010	35	0	3	0	0	0	38
2011	46	0	3	1	0	1	51
2012	62	0	1	0	0	0	63
2013	50	0	0	0	1	0	51
2014	51	0	4	0	1	0	56
2015	44	0	5	1	2	0	52
2016	55	1	5	1	0	0	62
2017	72	0	1	1	1	0	75
2018	7	0	0	0	1	0	8
Total	876	5	37	25	7	2	952
Cases with definite & probable diagnosis to date.

CJD Cases by Province/Territory May 31, 2018
Provinces	Total CJD Cases^{figure table note 1}	CJD Cases %^{figure table note 2}	% Expected (Difference)^{figure table note 3}
Newfoundland & Labrador	18	1.9	131.2%
Prince Edward Island	2	0.2	50.7%
Nova Scotia	35	3.7	141.5%
New Brunswick	27	2.8	137.0%
Quebec	230	24.2	105.7%
Ontario	339	35.6	92.1%
Manitoba	39	4.1	112.4%
Saskatchewan	38	4.0	125.9%
Alberta	99	10.4	89.1%
British Columbia	125	13.1	100.1%
Yukon	0.0	0.0	0.0%
Northwest Territories	0.0	0.0	0.0%
Nunavut	0.0	0.0	0.0%
Figure table notes Figure table note 1 Actual CJD n=952 Return to figure table note 1 referrer Figure table note 2 Actual % CJD Return to figure table note 2 referrer Figure table note 3 % of Predicted CJD (based on 2017 population) Return to figure table note 3 referrer Data includes both deceased and alive cases

Incidence of CJD Deaths Reported by CJDSS in Canada
As of May 31, 2018
Year of Death	Total CJD Cases	Population of Canada	Incidence Rate
1999	32	30,492,106	1.05
2000	35	30,783,969	1.14
2001	30	31,130,030	0.96
2002	36	31,450,443	1.14
2003	29	31,734,851	0.91
2004	44	32,037,434	1.37
2005	44	32,352,233	1.36
2006	44	32,678,986	1.35
2007	39	33,001,076	1.18
2008	49	33,371,810	1.47
2009	53	33,756,714	1.57
2010	38	34,131,451	1.11
2011	51	34,472,304	1.48
2012	63	34,880,248	1.81
2013	51	35,289,003	1.45
2014	56	35,675,834	1.57
2015	52	35,702,707	1.46
2016	62	36,286,400	1.71
2017	75	36,546,956	2.05
2018	8	36,708,083	0.52
Cases with definite & probable diagnosis to date. 2017 Population Source: Statistics Canada, CANSIM, table 051-0005