Creutzfeldt-Jakob disease surveillance system (CJDSS) report

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Referrals of suspected CJD reported by CJDSS, 1998-2023
As of August 31, 2023
Year of reporting Number of referrals
1998 43
1999 63
2000 82
2001 101
2002 103
2003 75
2004 90
2005 97
2006 80
2007 101
2008 100
2009 104
2010 76
2011 102
2012 103
2013 99
2014 99
2015 98
2016 117
2017 116
2018 125
2019 142
2020 123
2021 140
2022 162
2023 101
Total 2640
Definite and probable CJD, 1998-2023
As of 31 July, 2023
Year Sporadic Iatrogenic Genetic vCJD Total
1998 22 1 1 0 24
1999 27 2 3 0 32
2000 32 0 3 0 35
2001 27 0 3 0 30
2002 30 0 5 1 36
2003 27 1 1 0 29
2004 42 0 4 0 44
2005 42 0 2 0 44
2006 39 0 5 0 44
2007 35 0 4 0 39
2008 48 0 1 0 49
2009 48 0 5 0 53
2010 35 0 3 0 38
2011 46 0 4 1 51
2012 62 0 1 0 63
2013 50 0 1 0 51
2014 51 0 5 0 56
2015 44 0 8 0 52
2016 57 1 6 0 64
2017 82 0 5 0 87
2018 75 1 5 0 81
2019 76 0 3 0 79
2020 65 0 4 0 69
2021 60 0 3 0 63
2022 88 0 2 0 90
2023 40 0 0 0 40
Total 1250 6 85 2 1343

Cases with definite and probable diagnosis to date

CJD Cases by Province/Territory August 31, 2023
CJD Cases by Province/Territory August 31, 2023
Text Description
CJD Cases by Province/Territory August 31, 2023
Provinces Total CJD Cases
Newfoundland & Labrador 18
Prince Edward Island 4
Nova Scotia 45
New Brunswick 43
Quebec 348
Ontario 468
Manitoba 50
Saskatchewan 46
Alberta 136
British Columbia 183
Yukon 2
Northwest Territories 0.0
Nunavut 0.0

National total: 1343

Provincial totals of definite & probable CJD

*Canadian CJD surveillance began in 1998
Return to CJD Cases by Province/Territory 31 July, 2023

CJD deaths in Canada
Year of death Total CJD cases Population of Canada Crude mortality rate
1998 24 30,244,982 0.79
1999 32 30,492,106 1.05
2000 35 30,783,969 1.14
2001 30 31,130,030 0.96
2002 36 31,450,443 1.14
2003 29 31,734,851 0.91
2004 44 32,037,434 1.37
2005 44 32,352,233 1.36
2006 44 32,678,986 1.35
2007 39 33,001,076 1.18
2008 49 33,371,810 1.47
2009 53 33,756,714 1.57
2010 38 34,131,451 1.11
2011 51 34,472,304 1.48
2012 63 34,880,248 1.81
2013 51 35,289,003 1.45
2014 56 35,675,834 1.57
2015 52 35,702,707 1.46
2016 64 36,286,400 1.76
2017 86 36,712,658 2.37
2018 80 37,589,262 2.15
2019 79 37,811,399 2.09
2020 69 38,033,014 1.81
2021 63 38,929,902 1.62
2022 90 39,292,355 2.31
Cases with definite and probable diagnosis to date
Population estimates as of Q3 2022 (Statistics Canada population estimates, quarterly)

Related links

European Creutzfeldt Jakob Disease Surveillance Network

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